Caracterização de habilidades lingüísticas de crianças e adolescentes com Síndrome de Williams-Beuren

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dc.contributor.advisorCarreiro, Luiz Renato Rodriguespt_BR
dc.contributor.advisor1Latteshttp://lattes.cnpq.br/0203967709311323por
dc.contributor.authorSegin, Miriampt_BR
dc.creator.Latteshttp://lattes.cnpq.br/4433240490474925por
dc.date.accessioned2016-03-15T19:39:35Z
dc.date.accessioned2020-03-19T15:19:49Z
dc.date.available2011-01-18pt_BR
dc.date.available2020-03-19T15:19:49Z
dc.date.issued2010-08-25pt_BR
dc.description.abstractWilliams-Beuren Syndrome (WBS) is a genetic affection determined by the microdelation of contiguous genes in 7q11.23. The genetic profile of WBS is characterized by the visualconstructive deficit that contrasts with the good performance in verbal tasks, which sustains the hypothesis of dissociation between these abilities. This grants the syndrome peculiar cognitive and behavioral frames. The objective of this research is to describe the pattern of competences in tasks of linguistic abilities in 22 children and adolescents with WBS, aged between 7and 18 (M=11,6; DP=3,7), students of the 1st to 6th grades of elementary and special schools. We used the following instruments: WISC-III (to evaluate intellectual abilities); Wisconsin (used in neuropsychological assessment of abstract reasoning and cognitive strategies); CBCL/6-18 (behavioral assessment); Token-Comp (TT) used to working memory assessment; Peabody Picture Vocabulary Test (PPVT) used to receptive language assessment; Phonological Awareness by Oral Production Test; Syntactic Awareness Test; Word-Reading Efficiency Test; Test of Naming Images by Choosing Words; Test of Naming Images by Writing. The results of WISC-III, Wisconsin and CBCL/6-18 demonstrate mild to moderate intellectual disability, difficulty in concentration and identification of patterns of change, emotional and relationship problems, lack of attention, behavior disorders, challenge and opposition and somatic complaints. The results of TT and PPVT show that the receptive vocabulary is below expected for the level of schooling and age, and is close to the data found in 4-year-old-children. In the abilities of phonological and syntactic awareness, results indicate great deficiencies, with performances equivalent to those of 3-year-old children at the Phonological Awareness by Oral Production Test and of 4-year-olds at the Syntactic Awareness Test. No progression was found according to the increase of school grade. The tests Word-Reading Efficiency, Naming Images by Choosing Words and Naming Images by Writing were taken by 4 participants that presented deficits in the reading ability with graphophonemic decoding. They make more orthographic and semantic mistakes and show low capacity of naming by writing. Thus, it was possible to verify that the sample presents deficits in receptive language and work memory, difficulties in phonological and syntactic processing tasks, which are important factors to the proper development of the capacity to read and writeeng
dc.formatapplication/pdfpor
dc.identifier.urihttp://dspace.mackenzie.br/handle/10899/22458
dc.languageporpor
dc.publisherUniversidade Presbiteriana Mackenziepor
dc.rightsAcesso Abertopor
dc.subjectSíndrome de Williams-Beurenpor
dc.subjecthabilidade intelectualpor
dc.subjectperfil comportamentalpor
dc.subjectlinguagem receptivapor
dc.subjectconsciência fonológicapor
dc.subjectconsciência sintáticapor
dc.subjectleitura e escritapor
dc.subjectWilliams-Beuren Syndromeeng
dc.subjectintellectual abilityeng
dc.subjectbehavioral profileeng
dc.subjectreceptive languageeng
dc.subjectphonological awarenesseng
dc.subjectsyntactic awarenesseng
dc.subjectread and writeeng
dc.subject.cnpqCNPQ::CIENCIAS HUMANAS::PSICOLOGIApor
dc.thumbnail.urlhttp://tede.mackenzie.br/jspui/retrieve/3688/Miriam%20Segin.pdf.jpg*
dc.titleCaracterização de habilidades lingüísticas de crianças e adolescentes com Síndrome de Williams-Beurenpor
dc.typeDissertaçãopor
local.contributor.board1Macedo, Elizeu Coutinho dept_BR
local.contributor.board1Latteshttp://lattes.cnpq.br/0683719309513445por
local.contributor.board2Navas, Ana Luiza Gomes Pintopt_BR
local.contributor.board2Latteshttp://lattes.cnpq.br/0754347427711718por
local.publisher.countryBRpor
local.publisher.departmentPsicologiapor
local.publisher.initialsUPMpor
local.publisher.programDistúrbios do Desenvolvimentopor
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